{"id":6835,"date":"2025-10-21T20:16:55","date_gmt":"2025-10-21T20:16:55","guid":{"rendered":"https:\/\/ramib.org\/oficial\/?p=6835"},"modified":"2025-11-16T17:27:04","modified_gmt":"2025-11-16T17:27:04","slug":"04-11-2025-desafiaments-clinics-actuals-en-el-diagnostic-i-tractament-dimmunodeficiencies-primaries-i-secundaries","status":"publish","type":"post","link":"https:\/\/ramib.org\/oficial\/index.php\/2025\/10\/21\/04-11-2025-desafiaments-clinics-actuals-en-el-diagnostic-i-tractament-dimmunodeficiencies-primaries-i-secundaries\/","title":{"rendered":"04\/11\/2025: &#8220;Desafiaments cl\u00ednics actuals en el diagn\u00f2stic i tractament d&#8217;immunodefici\u00e8ncies prim\u00e0ries i secund\u00e0ries"},"content":{"rendered":"\n<p>l passat 4 de novembre, la Reial Acad\u00e8mia de Medicina dels Illes Balears va acollir una interessant sessi\u00f3 cient\u00edfica a c\u00e0rrec del Dr. Jaume Pons de Ves, centrada en el diagn\u00f2stic i tractament de les immunodefici\u00e8ncies i en l&#8217;\u00fas adequat dels antibi\u00f2tics.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-1024x682.jpg\" alt=\"\" class=\"wp-image-6863\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr-Pons-1.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>Va obrir l&#8217;acte el president de la corporaci\u00f3, Excm. Sr. Joan Besalduch Vidal, agraint als assistents la seva pres\u00e8ncia i al ponent la realitzaci\u00f3 de la sessi\u00f3.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-1024x682.jpg\" alt=\"\" class=\"wp-image-6865\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-2.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>L&#8217;encarregat de presentar el curr\u00edculum del ponent va ser l&#8217;acad\u00e8mic numerari M. Il\u00b7ltre. Sr. Jordi Reina Prieto.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-1024x682.jpg\" alt=\"\" class=\"wp-image-6871\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-5.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>En la seva pon\u00e8ncia, el Dr. Pons va explicar que les immunodefici\u00e8ncies \u2014ara denominades \u00aberrors cong\u00e8nits de la immunitat\u00bb\u2014 engloben m\u00e9s de 500 trastorns distints que afecten el desenvolupament o funcionament del sistema immunitari. Va subratllar que, a m\u00e9s d&#8217;una major susceptibilitat a infeccions, aquests pacients poden presentar autoimmunitat, inflamaci\u00f3, al\u00b7l\u00e8rgies o major risc de neopl\u00e0sies.<\/p>\n\n\n\n<p>Va diferenciar les immunodefici\u00e8ncies prim\u00e0ries (d&#8217;origen gen\u00e8tic) de les secund\u00e0ries (que apareixen al llarg de la vida per altres malalties, tractaments o envelliment).<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-1024x682.jpg\" alt=\"\" class=\"wp-image-6873\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-6.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>Va destacar la import\u00e0ncia d&#8217;una hist\u00f2ria cl\u00ednica rigorosa, al costat d&#8217;estudis de laboratori i gen\u00e8tica, per a realitzar un diagn\u00f2stic preco\u00e7. A Balears, la unitat d&#8217;Immunologia porta m\u00e9s de 40 anys dedicada a aquests estudis.<\/p>\n\n\n\n<p>Aix\u00ed mateix, va alertar sobre un aspecte de gran inter\u00e8s per a tot l&#8217;\u00e0mbit sanitari i la poblaci\u00f3: la correcta administraci\u00f3 d&#8217;antibi\u00f2tics. Va indicar que els antibi\u00f2tics s\u00f3n fonamentals, per\u00f2 que quan s&#8217;usen de manera incorrecta \u2014per exemple sense indicaci\u00f3, malament pauta o interrupci\u00f3 prematura\u2014 poden fomentar l&#8217;aparici\u00f3 de bacteris resistents, la qual cosa agreuja el problema de les infeccions tant en persones amb immunodefici\u00e8ncies com en la poblaci\u00f3 general.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-1024x682.jpg\" alt=\"\" class=\"wp-image-6869\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-pons-4.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>El Dr. Pons va incidir en qu\u00e8, en casos d&#8217;immunodefici\u00e8ncia, el retard en el diagn\u00f2stic o la fallada a prevenir infeccions repetides pot portar a mal pulmonar o a deterioraci\u00f3 de la funci\u00f3 respirat\u00f2ria.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-1024x682.jpg\" alt=\"\" class=\"wp-image-6875\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-7.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>Quant a tractament, va assenyalar que en la majoria dels casos el d\u00e8ficit \u00e9s d&#8217;anticossos, i que el tractament habitual inclou immunoglobulines, antibi\u00f2tics terap\u00e8utics o preventius, i vacunes. En algunes formes greus, es contempla trasplantament de medul\u00b7la \u00f2ssia i, encara que de forma encara emergent, ter\u00e0pia g\u00e8nica.<\/p>\n\n\n\n<p>Aquesta confer\u00e8ncia va permetre visibilitzar un doble desafiament sanitari: d&#8217;una banda, el reconeixement i tractament adequat de les immunodefici\u00e8ncies com a part essencial del servei de salut; i per un altre, la necessitat d&#8217;una gesti\u00f3 responsable dels antibi\u00f2tics per a evitar la creixent amena\u00e7a de la resist\u00e8ncia bacteriana. L&#8217;acte va consolidar aix\u00ed un espai de reflexi\u00f3 per a professionals sanitaris i gestors p\u00fablics a Balears.<\/p>\n\n\n<div class=\"wp-block-image\">\n<figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"1024\" height=\"682\" src=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-1024x682.jpg\" alt=\"\" class=\"wp-image-6877\" srcset=\"https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-1024x682.jpg 1024w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-300x200.jpg 300w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-768x512.jpg 768w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-1536x1024.jpg 1536w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-696x464.jpg 696w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-1068x712.jpg 1068w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-630x420.jpg 630w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8-1920x1280.jpg 1920w, https:\/\/ramib.org\/oficial\/wp-content\/uploads\/2025\/10\/Dr.-Pons-8.jpg 2000w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/><\/figure><\/div>\n\n\n<p>Pot visualitzar la sessi\u00f3 en el canal de youtube de la corporaci\u00f3:<\/p>\n\n\n\n<figure class=\"wp-block-embed aligncenter is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<iframe loading=\"lazy\" title=\"Desaf\u00edos cl\u00ednicos en el diagn\u00f3stico y tratamiento de inmunodeficiencias primarias y secundarias\" width=\"696\" height=\"392\" src=\"https:\/\/www.youtube.com\/embed\/8evnmOHnGng?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe>\n<\/div><\/figure>\n","protected":false},"excerpt":{"rendered":"<p>l passat 4 de novembre, la Reial Acad\u00e8mia de Medicina dels Illes Balears va acollir una interessant sessi\u00f3 cient\u00edfica a c\u00e0rrec del Dr. Jaume Pons de Ves, centrada en el [&hellip;]<\/p>\n","protected":false},"author":3,"featured_media":6879,"comment_status":"open","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"categories":[14,24,1274,17],"tags":[1642,1640,1632,1647,1641,1638,1637,1633,1634,1646,1648,1639,1645,1636,1635,1631,1644,1643],"_links":{"self":[{"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/posts\/6835"}],"collection":[{"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/comments?post=6835"}],"version-history":[{"count":3,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/posts\/6835\/revisions"}],"predecessor-version":[{"id":6886,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/posts\/6835\/revisions\/6886"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/media\/6879"}],"wp:attachment":[{"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/media?parent=6835"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/categories?post=6835"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/ramib.org\/oficial\/index.php\/wp-json\/wp\/v2\/tags?post=6835"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}